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Research Article| Volume 21, ISSUE 1, P19-26, January 1966

Oral manifestations of Marfan's syndrome in twins

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      Abstract

      The dental aspects of Marfan's syndrome in a pair of identical twins have been described. The narrow dental arches and high palatal vaults seen in these patients seem to be a consistent feature of this disease but cannot be considered pathognomonic, since they may and do occur frequently in many mixed dentitions without any aberrant congenital connective tissue background. It may be of interest to conjecture, nevertheless, why arachnodactyly is so reflected in the oral structures. Is it a direct result of the genetic mutation? Or is it a response to functional and environmental stresses on growth and development associated with the component abnormalities? These are areas which require further study.
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