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Abstract
A report of a
child with severe congenital abnormalities consistent with a diagnosis of progeria
and associated with Camurati—Engelmann's disease has been presented. Interesting features
of the case were the marked sclerotic changes in, and increased density of, the ribs
and the mandible. The congenital craniostenoses have also been discussed. The dental
eruption appeared to be normal, although there was severe enamel hypoplasia 0 an Angle
Class I occlusion and a posterior cross-bite.

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References
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Article info
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Copyright
© 1969 Published by Elsevier Inc.