Research Article| Volume 27, ISSUE 1, P20-26, January 1969

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Multiple congenital abnormalities with diaphyseal dysplasia (Camurati—Engelmann's syndrome)

Report of a case
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      A report of a Math Eq child with severe congenital abnormalities consistent with a diagnosis of progeria and associated with Camurati—Engelmann's disease has been presented. Interesting features of the case were the marked sclerotic changes in, and increased density of, the ribs and the mandible. The congenital craniostenoses have also been discussed. The dental eruption appeared to be normal, although there was severe enamel hypoplasia 0 an Angle Class I occlusion and a posterior cross-bite.
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