Abstract
Klippel-Trénaunay syndrome was first reported in 1900 by Klippel and Trénaunay. The
syndrome is characterized by the triad of vascular nevi, venous varicosity, and hyperplasia
of soft tissue—and possibly bone—in the affected area. The original description was
made with regard to the extremities. The syndrome is diagnosed on the basis of 2 or
3 symptoms. The 3 patients reported here presented with hemangioma and hypertrophy
of the jawbone and concomitant malocclusion. There were clinically no obvious varicose
veins. It appears that gravity plays an important role in the venous drainage from
the head and neck region, and this could be the reason for the rarity of varicose
veins in the head and neck region when compared with lower extremities. In addition,
2 of the 3 cases showed exophytic pedunculated growth arising from the gingiva, which
has not been reported in any previous case reports. The following report presents
the clinical features in the orofacial region and highlights the clinical significance
of this syndrome. (Oral Surg Oral Med Oral Pathol Oral Radiol Endod 2002;93:276-80)
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References
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Article info
Publication history
Accepted:
July 18,
2001
Received in revised form:
March 15,
2001
Received:
January 24,
2001
Footnotes
*Reprint requests Renuka J. Bathi, MDS, Department of Oral Medicine and Radiology, S. D. M. College of Dental Sciences, Dharwad, Karnataka-580009, India
Identification
Copyright
© 2002 Mosby, Inc. Published by Elsevier Inc. All rights reserved.
